以肝衰竭为主要表现的噬血细胞综合征1例报告

罗利婷; 张霞; 马鹤铭; 任天棋; 曹鹤; 牛俊奇

doi:10.3969/j.issn.1001-5256.2020.02.038

以肝衰竭为主要表现的噬血细胞综合征1例报告

DOI: 10.3969/j.issn.1001-5256.2020.02.038

1. 吉林大学第一医院肝胆胰内科
2. 吉林大学第一医院肿瘤中心血液科

基金项目:

吉林大学高层次科技创新团队建设项目与高等院校基本科研业务费(2017TD-08)；

详细信息

中图分类号: R575.3;R55
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出版历程
- 出版日期: 2020-02-20

A case of hemophagocytic syndrome with liver failure as the main manifestation

Department of Hepatology,The First Hospital of Jilin University

Research funding:

摘要

摘要:
<正>1病例资料患者女性,37岁,主因"发热2月余,尿黄1月、目黄半月,腹胀、双下肢水肿5 d"于2013年7月8日入本院。既往:否认肝炎病史,无烟酒嗜好。入院查体:体温36. 5℃,皮肤、巩膜重度黄染,颜面部中度水肿,未见肝掌、蜘蛛痣。腹轻度膨隆,正中腹部压痛,无反跳痛及肌紧张,脾肋下3 cm,移动性浊音阳性,双下肢中度水肿。入院后患者发热2次,最高体温达38. 5℃。辅助检查血常规:白细胞8. 68×109/L,中性粒细胞6. 68×109/L,血红蛋白115 g/L,血小板31×109/L。
- 肝功能衰竭 /
- 淋巴组织细胞增多症,嗜血细胞性 /
- 诊断
- liver failure /
- lymphohistiocytosis,hemophagocytic /
- diagnosis

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参考文献(10)

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[8] YIN NN,PU L,XIANG P,et al. A case report of hemophagocytic lymphohistiocytosis first presenting as liver injury during pregnancy[J/CD]. Chin J Liver Dis(Electronic Version),2018,10(1):78-82.(in Chinese)尹宁宁，蒲琳，向攀，等．以肝功能损伤为首发表现的妊娠合并噬血细胞综合征1例[J/CD]．中国肝脏病杂志(电子版)，2018,10(1):78-82.

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