自身免疫性肝病重叠综合征的研究现状

倪萍; 凡小丽; 杨丽

doi:10.3969/j.issn.1001-5256.2020.04.006

自身免疫性肝病重叠综合征的研究现状

DOI: 10.3969/j.issn.1001-5256.2020.04.006

四川大学华西医院消化内科

基金项目:

国家自然科学基金面上项目(81770568)；

详细信息

中图分类号: R575
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出版历程
- 收稿日期: 2020-03-04
- 出版日期: 2020-04-20

Current status of research on overlap syndrome of autoimmune liver disease

Department of Gastroenterology,West China Hospital,Sichuan University

Research funding:

摘要

摘要: 自身免疫性肝病主要包括原发性胆汁性胆管炎（PBC）、自身免疫性肝炎（AIH）和原发性硬化性胆管炎（PSC）。同时或相继出现以上任意两种单独自身免疫性肝病特征者称为重叠综合征。其中,以PBC重叠AIH（PBC-AIH）相对最为常见。若不及时接受治疗可迅速进展至肝硬化和肝衰竭。就近年自身免疫性肝病重叠综合征的研究进展进行了总结。
- 胆管炎,硬化性 /
- 肝硬化,胆汁性 /
- 肝炎,自身免疫性 /
- 重叠综合征
Abstract: Autoimmune liver diseases mainly include primary biliary cholangitis( PBC),autoimmune hepatitis( AIH),and primary sclerosing cholangitis. Simultaneous or successive occurrence of the features of any two of the above diseases is called overlap syndrome,among which PBC-AIH overlap syndrome is the most common type. Overlap syndrome can progress rapidly to liver cirrhosis and liver failure without timely treatment. This article summarizes the research advances in overlap syndrome of autoimmune liver disease in recent years.
- cholangitis,sclerosing /
- liver cirrhosis,biliary /
- hepatitis,autoimmune /
- overlap syndrome

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参考文献(57)

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