PDF下载 ( 927 KB)
A case of idiopathic non-cirrhotic portal hypertension with hepatic encephalopathy as the first symptom
-
摘要:
<正>门静脉高压症是指由于门静脉压力持续增高引发的一系列症候群,主要表现为腹水、门-腔侧支循环开放、脾功能亢进及脾大等,其最常见原因为肝硬化,约占90%左右,然而,非肝硬化性门静脉高压只占10%左右,其主要分为慢性门静脉血栓形成和特发性非肝硬化门静脉高压,其中特发性非肝硬化门静脉高压更为罕见,其是一种病因不明,且由非肝硬化因素所致的肝内门静脉闭塞所引起的肝脏血管疾病,主要表现为肝内型门静脉高压,其显著特点是肝功能正常或接近正常。静脉曲张破裂出血是其最常见且致死率极高的一种并发症,而以肝性脑病为并发症的则更为罕见[1]。
-
关键词:
- 特发性非肝硬化性门静脉高压 /
- 肝性脑病 /
- 活组织检查
-
[1] SAVERIA I,MUSTIKA S. An 18-year-old man with idiopathic non-cirrhotic portal hypertension[J]. Acta Med Indones,2019,51(2):165-168. [2] NICOLETTI V,GIOIA S,LUCATELLI P,et al. Hepatic encephalopathy in patients with non-cirrhotic portal hypertension:Description,prevalence and risk factors[J]. Dig Liver Dis,2016,48(9):1072-1077. [3] ZHAO LH,JIA JD. Idiopathic non-cirrhosis portal hypertension[J]. Chin Hepatol,2019,24(3):219-221.(in Chinese)赵连晖，贾继东．特发性非肝硬化性门脉高压[J]．肝脏，2019,24(3):219-221. [4] European Association for the Study of the Liver. EASL clinical practice guidelines:Vascular diseases of the liver[J]. J Hepatol,2016,64(1):179-202. [5] SIRAMOLPIWAT S,SEIJO S,MIQUEL R,et al. Idiopathic portal hypertension:Natural history and long-term outcome[J].Hepatology,2014,59(6):2276-2285. [6] XU H,ZHANG F,ZHANG M,et al. Effect of propranolol on hemodynamics and its clinical significance in patients with portal hypertension[J]. J Clin Hepatol,2019,35(4):801-807.(in Chinese)徐慧，张峰，张明，等．普萘洛尔对肝硬化门静脉高压患者血流动力学的影响和疗效观察[J]．临床肝胆病杂志，2019,35(4):801-807. [7] SARIN SK,GUPTA N,JHA SK,et al. Equal efficacy of endoscopic variceal ligation and propranolol in preventing variceal bleeding in patients with noncirrhotic portal hypertension[J].Gastroenterology,2010,139(4):1238-1245. -
本文二维码
计量
- 文章访问数: 515
- HTML全文浏览量: 7
- PDF下载量: 94
- 被引次数: 0
下载:
