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ISSN 1001-5256 (Print)
ISSN 2097-3497 (Online)
CN 22-1108/R
Volume 36 Issue 6
Jun.  2020
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Article Contents

Research advances in primary biliary cholangitis with extrahepatic autoimmune diseases

DOI: 10.3969/j.issn.1001-5256.2020.06.046
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  • Published Date: 2020-06-20
  • Primary biliary cholangitis( PBC) is a chronic autoimmune liver disease characterized by progressive destruction of the small intrahepatic bile ducts. Patients with PBC often have extrahepatic autoimmune diseases,which can involve multiple organs and systems including the gastrointestinal tract,lung,rheumatoid immune system,and endocrine system. This article summarizes the research advances in the disease spectrum,pathogenesis,treatment,and prognosis of PBC with extrahepatic autoimmune disease.

     

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