中文English
ISSN 1001-5256 (Print)
ISSN 2097-3497 (Online)
CN 22-1108/R

留言板

尊敬的读者、作者、审稿人, 关于本刊的投稿、审稿、编辑和出版的任何问题, 您可以本页添加留言。我们将尽快给您答复。谢谢您的支持!

姓名
邮箱
手机号码
标题
留言内容
验证码

婴儿胆汁淤积症的鉴别诊断思路

朱启镕 王建设

引用本文:
Citation:

婴儿胆汁淤积症的鉴别诊断思路

详细信息
  • 中图分类号: R725.7

Differential diagnosis of infantile cholestasis

  • 摘要: 胆汁淤积是婴儿肝脏疾病最常见的临床表现。病因在很大程度上决定其预后,有些病因需要医生做出快速的诊断及采取恰当的治疗。胆道闭锁、败血症、尿路感染、甲状腺功能低下、Citrin缺陷病、酪氨酸血症及先天性胆汁酸合成缺陷都要及早诊断,因为对这些疾病及时适当的治疗可显著的改善预后。

     

  • [1]朱启镕, 王晓红, 王建设.婴儿肝病综合征诊治修订方案[J].中华传染病杂志, 2004, 22 (5) :357.
    [2]Moyer V, Freese DK, Whitington PF, et al.Guideline for theevaluation of cholestasis jaundice in infants:recommendationsof the North American Society for Pediatric Gastroenterology, Hepatology and Nutrition[J].J Pediatr Gastroenterol Nutr, 2004, 39 (2) :115-128.
    [3]Hartley JL, Davenport M, Kelly DA.Biliary atresia[J].Lancet, 2009, 374 (9702) :1704-1713.
    [4]Hsiao CH, Chang MH, Chen HL, et al.Universal screeningfor biliary atresia using an infant stool color card in Taiwan[J].Hepatology, 2008, 47 (4) :1233-1240.
    [5]Zhou J, Shen Z, He Y, et al.The current status of pediatric livertransplantation in Mainland China[J].Pediatr Transplant, 2010, 14 (5) :575-582.
    [6]Serinet MO, Wildhaber BE, BrouéP, et al.Impact of age atKasai operation on its results in late childhood and adolescence:a rational basis for biliary atresia screening[J].Pediatrics, 2009, 123 (5) :1280-1286.
    [7]Fu HY, Zhang SR, Yu H, et al.Most common SLC25A13 mutationin 400 Chinese infants with intrahepatic cholestasis[J].World JGastroenterol, 2010, 16 (18) :2278-2282.
    [8]方玲娟, 王建设.先天性胆汁酸合成障碍及胆汁淤积性肝病[J].临床肝胆病杂志, 2010, 26 (6) :585-588.
    [9]Gonzales E, Gerhardt MF, Fabre M, et al.Oral cholic acid forhereditary defects of primary bile acid synthesis:a safe andeffective long-term therapy[J].Gastroenterology, 2009, 137 (4) :1310-1320.
    [10]Pierre G, Setchell K, Blyth J, et al.Prospective treatment ofcerebrotendinous xanthomatosis with cholic acid therapy[J].JInherit Metab Dis.2008 Dec 27.[Epub ahead of print]
  • 加载中
计量
  • 文章访问数:  3061
  • HTML全文浏览量:  16
  • PDF下载量:  1268
  • 被引次数: 0
出版历程
  • 收稿日期:  2011-03-29
  • 出版日期:  2011-07-20
  • 分享
  • 用微信扫码二维码

    分享至好友和朋友圈

目录

    /

    返回文章
    返回