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ISSN 1001-5256 (Print)
ISSN 2097-3497 (Online)
CN 22-1108/R
Volume 39 Issue 11
Nov.  2023
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Article Contents

Transcatheter closure of rare type Ⅱ Abernethy malformation with pulmonary hypertension in children: A case report

DOI: 10.3969/j.issn.1001-5256.2023.11.022
Research funding:

Fund Project of Hubei Chen Xiaoping Science and Technology Development Foundation (CXPJJH11800001-2018246)

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  • Corresponding author: ZHANG Heng, zhangheng9987@163.com (ORCID: 0000-0003-2243-9279)
  • Received Date: 2023-06-27
  • Accepted Date: 2023-07-28
  • Published Date: 2023-11-28
  • Abernethy malformation, also known as congenital portosystemic shunts, is rare in clinical practice, with less than 300 cases reported in the global literature up to 2019. The disease can have serious complications such as pulmonary hypertension, liver tumor, and liver failure and tends to have an extremely poor prognosis, and early diagnosis and active and effective treatment can reduce and delay the onset of complications. In this case, portography combined with balloon occlusion helped to display the underdeveloped slender portal vein with dysplasia, so that the child who was formerly misdiagnosed with type Ⅰ Abernethy malformation was diagnosed with type Ⅱ Abernethy malformation, and then the child was successfully treated by transcatheter closure. This article gives a detailed report of this case.

     

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