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介入封堵治疗小儿Ⅱ型Abernethy畸形合并肺动脉高压1例报告

张恒 江斌 方志成 孟忠吉 杜恩辅

引用本文:
Citation:

介入封堵治疗小儿Ⅱ型Abernethy畸形合并肺动脉高压1例报告

DOI: 10.3969/j.issn.1001-5256.2023.11.022
基金项目: 

湖北陈孝平科技发展基金会基金项目 (CXPJJH11800001-2018246)

伦理学声明:本例报告已获得患者家属知情同意。
利益冲突声明:本文不存在任何利益冲突。
作者贡献声明:张恒负责课题设计,资料分析,撰写论文;方志成、孟忠吉、杜恩辅参与收集数据,修改论文;江斌负责拟定写作思路,指导撰写文章并最后定稿。
详细信息
    通信作者:

    张恒, zhangheng9987@163.com (ORCID: 0000-0003-2243-9279)

Transcatheter closure of rare type Ⅱ Abernethy malformation with pulmonary hypertension in children: A case report

Research funding: 

Fund Project of Hubei Chen Xiaoping Science and Technology Development Foundation (CXPJJH11800001-2018246)

More Information
  • 摘要: Abernethy又称先天性门体静脉分流畸形,临床罕见,截至2019年全球文献报道不足300例,该病可合并肺动脉高压、肝脏肿瘤、肝衰竭等严重并发症,总体预后极差,早期诊断、积极有效治疗可降低和延缓并发症发生。本文通过门静脉造影,结合球囊阻断,将原本发育不良、纤细未显影的门静脉显影,从而将原本误诊为Ⅰ型Abernethy畸形的患儿明确为Ⅱ型Abernethy畸形,进而经介入封堵治疗成功救治患儿,现报道如下。

     

  • 图  1  腹部增强CT 检查

    注::a,冠状位;b,矢状位;c,动脉期;d,门静脉期;e,延迟期。

    Figure  1.  The enhanced CT images

    图  2  下腔静脉、门静脉造影术及试验性球囊封堵术

    注: a,下腔静脉、门静脉造影;b,肝静脉造影;c,球囊封堵后门静脉造影;d,门静脉主干与髂内静脉交通支。

    Figure  2.  The portography and experimental balloon occlusion

    图  3  术后门静脉CT检查

    注: a,术后VR图像;b,术后MIP图像。

    Figure  3.  Postoperative portal vein CT images

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出版历程
  • 收稿日期:  2023-06-27
  • 录用日期:  2023-07-28
  • 出版日期:  2023-11-28
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